ICD Coding

One difficulty researchers have encountered in trying to calculate the number of CCM cases is significant variation in ICD coding of the disorder. ICD is the system used by healthcare providers to classify and code diagnoses.

The Angioma Alliance Scientific Advisory Board has suggested a consensus code moving forward to allow for better tracking. In order to increase sensitivity and specificity, we request that clinicians use the following ICD coding for their cerebral cavernous malformation patients:

ICD-9 code:

228.02  Hemangioma of Intracranial Structures


In ICD-10, this code converts to:

D18.02 Hemangioma of Intracranial Structures